Caroli Disease
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New findings in liver disease in children described from University of Medicine
2009 JUN 1 - (NewsRx.com) -- A new study, 'Fibropolycystic liver disease in children,' is now available. "Fibropolycystic liver diseases are a group of associated congenital disorders that present most often in childhood. These disorders include congenital hepatic fibrosis, biliary hamartomas, autosomal dominant polycystic liver disease, choledochal cysts and Caroli disease," scientists in the United States report. "We present a discussion and illustrations of the embryology, genetics, anatomy, pathology, imaging approach and key imaging features that distinguish fibropolycystic liver disease in children. The pathogenesis of these disorders is believed to be abnormal development of the embryonic ductal plates, which ultimately form the liver and biliary systems," wrote M.C. Veigel and colleagues, University of Medicine. The researchers concluded: "An understanding of the abnormal embryogenesis helps to explain the characteristic imaging features of these disorders." Veigel and colleagues published their study in Pediatric Radiology (Fibropolycystic liver disease in children. Pediatric Radiology, 2009;39(4):317-27; quiz 420-1). For additional information, contact M.C. Veigel, Kansas City University of Medicine & Biosciences, Kansas City, MO USA.. The publisher's contact information for the journal Pediatric Radiology is: Springer, 233 Spring Street, New York, NY 10013, USA. Keywords: United States, Kansas City, Anatomy, And Neonatal Disease And Abnormalities, Caroli Disease, Choledochal Cyst, Congenital Hepatic Fibrosis, Cysts, Embryology, Gastroenterology, Genetics, Hepatology, Hereditary, Liver Disease, Pathology, Pediatric, Pediatrics, Radiology. This article was prepared by Gastroenterology Week editors from staff and other reports. Copyright 2009, Gastroenterology Week via NewsRx.com.
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